Hemosiderosis pulmonar idiopática en la infancia: buena respuesta al tratamiento con . Unidad de Neumología Pediátrica, Hospital Universitario Materno-. Idiopathic pulmonary hemosiderosis is a rare disease characterized by repeated episodes of bleeding into the lungs, which can cause anemia and lung disease. Abstract. PREGO, JAVIER and OTORMIN, MóNICA. Hemosiderosis pulmonar: Síndrome de Goodpasture. Arch. Pediatr. Urug. [online]. , vol, suppl.1, pp .
|Published (Last):||26 December 2011|
|PDF File Size:||10.7 Mb|
|ePub File Size:||13.28 Mb|
|Price:||Free* [*Free Regsitration Required]|
Monaldi Arch Chest Dis.
Hemosiderosis pulmonar idiopática: Evolución de 5 niños
A azatioprina foi mantida isoladamente. Idiopathic pulmonary haemosiderosis IPH is a rare and serious disorder characterised by diffuse alveolar haemorrhage. Idiopathic pulmonary haemosiderosis or idiopathic pulmonary hemosiderosis. SCS Quadra 1, Bl. Intial pulmonary CT were normal in 2, 2 had a pattern of alveolar infiltrates and one interstitial infiltrates, follow up CT scans remained normal in 2 patients and showed interstitial infiltrates in the rest.
Idiopathic pulmonary hemosiderosis treated with azathioprine.
Are you a health professional able to prescribe or dispense drugs? Pulmonary haemosiderosis in infants and children. Initial pulmonary function PFT tests were normal in 3, mildly restrictive in 1 and mildly obstructive in 1, however during the follow-up period there were changes in the PFT in 2 patients, from normal to mildly restrictive in 1 and from mildly to moderately obstructive in 1.
Budesonide inhalation to treat idiopathic pulmonary haemosiderosis. Antineutrophil cytoplasmic antibodies ANCA in idiopathic pulmonary hemosiderosis. Contudo, o acompanhamento da paciente por quatro anos afastou estas possibilidades, bem como a possibilidade de colagenoses e vasculites. Chloroquine in hemosidderosis pulmonary hemosiderosis. Summary idiopathic pulmonary hemosiderosis is those processes characterized by anomalous depots of hemosiderin in the pulmonary parenchyma, secondary to diffuse and repeated alveolar bleedings.
Continuing navigation will be considered as acceptance of this use. It is characterized by recurrent episodes of severe hypochromic anemia, alveolar bleeding, and typical radiologic findings.
Treatment of idiopathic pulmonary hemosiderosis with inhaled flunisolide. Pediatr Rio de J.
Idiopathic pulmonary hemosiderosis iph is a rare disorder of unknown etiology which can cause diffuse alveolar hemorrhage dah. We speculate that the use of inhaled steroids can reduce the secondary effects of oral steroids in IPH. Idiopathic pulmonary haemosiderosis in children: The Impact Factor measures the average number of citations received in a particular year by papers published in the journal during the two receding years.
CiteScore measures average citations received per document published. Secondary effects included hemosiderosjs in 5 children, Cushing syndrome in 3 and retrocapsular opacities in 2. Acute respiratory insufficiency as debut of idiopathic pulmonary hemosiderosis in an infant.
Idiopathic pulmonary hemosiderosis treated with azathioprine in a child
pulmonxr Hemosiderosis pulmonar embolia, infarto y hemorragia pulmonares atelectasia tumores pulmonares. Hemosiderin deposition in the lungs is often seen after diffuse alveolar hemorrhage, which occurs in diseases such as goodpastures syndrome, granulomatosis with polyangiitis, and idiopathic pulmonary hemosiderosis. Hemoptisis, hemorragia alveolar difusa, sindrome pulmonarrenal, hemosiderosis, corticoides, inmunosupresores.
You can change the settings or obtain more information by clicking here. Idiopathic pulmonary hemosiderosis should be included as a possible diagnosis of children with anemia and chronic lung disease.
One patient became pregnant without ill effects and delivered a healthy baby. J Pediatr Rio J. In december and januaryarticles in mmwr hemosidegosis a cluster of 10 infants from cleveland, ohio, with acute idiopathic pulmonary hemorrhage, also referred to as pulmonary hemosiderosis.
Pdf on dec 1,rodolfo burdach w and others published hemosiderosis pulmonar idiopatica h. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field.
There was a problem providing the content you requested
Hemosiderosis pulmonar idiopatica con osificacion pulmonar. There were no deaths. Its aetiology is unknown but owing to its unpredictable prognosis long term treatment is justified. After 5 years of treatment 2 children stopped having bleeding episodes, 3 had in general mild episodes in whom 2 had serious bleeding events, one needing mechanical ventilation.
The clinical course is exceedingly variable especially in children and a substantial proportion of this age group is undiagnosed.